Sturge weber syndrome: an exceptional cause of epilepsy in children (a case report)

Sturge-Weber syndrome (SWS) or encephalo-facial angiomatosis, is a rare congenital neuro-cutaneous and ocular syndrome. It comprises two types of malformations: congenital facial capillary angioma and leptomeningeal capillaro-venous angioma, most often homolateral parieto-occipital. The most frequent clinical neurological presentation is epileptic seizures. Magnetic resonance Imaging (MRI), plays an important role in establishing the diagnosis. We report a case of SSW grouping the different elements of the original triad: planar angioma of the hemiface, leptomeningeal angiomatosis and choroidal angioma with glaucoma.