Keratocystic odontogenic tumor are known for their peculiar behaviour, varied origin, debated development, unique tendency to recur and disputed treatment modalities. It was formerly known as odontogenic keratocyst (OKC). It received its new title as ‘Keratocystic odontogenic tumor’ (KCOT) by the who (2005) in order to suggest its aggressive and recurrent nature. It is a most common cyst, generally seen in men and most commonly occur in mandibular angle region and associated with basal cell nevus syndrome. KCOT is a benign intraosseous neoplasm of the jaw. Dentigerous cyst is odontogenic cyst commonly seen arising from impacted mandibular third molar.
We present a rare case of simultaneous occurrence of both these lesions in the same region. A male in the first decade of life reported with the complaint of swelling in anterior region of lower jaw. Clinical and radiographic findings were suggestive of a odontogenic keratocyst. Cystic lesion was enucleated with peripheral ostectomy and the specimen was sent for histopathological analysis. It showed KCOT in association with dentigerous cyst. This case is worth discussing as it is rare to find the simultaneous occurrence of two pathologies in the same region of jaw and there is no comment of the same in the literature. The common site for KCOT is mandibular angle and for DC impacted third molar. But in our case, two pathologies were found in the anterior mandible in association with an impacted canine.