A rare case of scleroderma in male

Scleroderma is an autoimmune connective tissue disorder. This condition can be localized or systemic. It mainly involves skin, blood vessel, and visceral organs. The term “sclera” meaning hard “derma” meaning skin in Greek. The manifestations are due to diffuse deposition of collagen in the skin and internal organs along with vascular injury and immunologic abnormalities. Its estimated prevalence is 250 cases in a million and occurs rarely in males. Salt and pepper and hyde leather skin are typical findings for a patient with scleroderma. The aim of this case report is to present a 29-year-old male patient who came to our hospital with complaints of difficulty in swallowing since 2 weeks. On examination all systems were normal, and he had salt and pepper type of skin pattern post auricular region, hyde leather like skin, shiny and dry, pinched up nose. He was worked up for Connective tissue disorder and was found to have scleroderma with esophageal dyskinesia. However, atypical about this case is patient is a male and anti topoisomerase and anti centromere were negative.