A nephrotic syndrome revealing kartagener’s syndrome complicated by renal amyloidosis

Kartagener’s syndrome is a group of primary ciliary dyskinesia associating situs inversus totalis, bronchiectasis and recurrent chronic sinusitis. It’s secondary to structural and functional ciliary abnormalities leading to impaired mucociliary clearance. It’s a rare genetic disorder transmitted in autosomal recessive mode (Prevalence 1/10000 to 1/20000).
We report a case of a 54 year-old-woman who was admitted for a nephrotic syndrome. Investigations revealed a Kartagener’s syndrome complicated by a renal amyloidosis. It’s a rare complication of Kartagener’s syndrome resulting probably from bronchiectasis and chronic respiratory infections.