Digital necrosis revealing sneddon syndrome

Sneddon’s syndrome is a rare disease defined by the presence of ischemic cerebrovascular events associated with livedo racemosa. It can also affect other organs such as heart, kidneys, eyes and the peripheral nervous system. We herein describe the case of a 28-year old man, who presented with Raynaud’s phenomenon, digital necrosis, neurological and cardiac manifestations revealing Sneddon syndrome. We highlight through this case diagnostic and therapeutic challenges of Sneddon syndrome.