Purpose: Craniofacial fibrous dysplasia is a benign slowly progressive disease in which normal craniofacial bones are replaced by immature fibro-osseous tissue. This case evaluates the need for early surgical intervention in such patients for its management and to stop further progression.
Methods and Materials: A 35yrs year old man with normal visual acuity and fundus finding presented with axial proptosis of left eye. On further evaluation by MDCT a diagnosis of craniofacial fibrous dysplasia involving left orbit was made. His rest ocular functions were normal including normal audiometric finding.
Result: Left frontal craniotomy followed by medial maxillectomy and
ethmoidectomy done on left front medial region with front medial osteotomy and debulking surgery. The specimen was further diagnosed as Fibrous Dysplasia involving bone. In periodic follow-up there was regression of proptosis. Initially there was diplopia in lateral gaze of left eye but subsequent follow-up resolved the complaint.
Conclusion: Early surgical intervention is needed to stop further progression. Periodic follow-up is recommended to monitor for recurrence and malignant transformation.
Impact Factor
2022: 6.012
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